Abstract

Scrotal leiomyosarcoma is seen rarely and may be paratesticular or intratesticular. An 18-year-old male, operated for paratesticular leiomyosarcoma 2 years before, was referred to our department with unresectable intraabdominal metastases. Combination chemotherapy regimen (ifosfamide with mesna protection and doxorubicin) was started and very good partial regression was achieved after 6 cycles. Our case highlighted that long-term follow-up of the patients with the paratesticular leiomyosarcoma is required and systemic chemotherapy might be very effective in metastatic setting.